PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented. Very few cases of gigantiform cementoma have been reported, and those associated with a positive family history are especially rare. Confusion exists about the. Familial gigantiform cementoma is a rare benign fibrocemento-osseous lesion of the jaws that can cause severe facial deformity. It has an.

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Surgery with recontouring and shaving intent was initially attempted in a local institution about 7 months ago, but in vain. We are determined to keep this website freely accessible.

Cemento-osseous dysplasia of the jaw bones: We might not hastily come to the conclusion that coexistence of FGC and polyostotic pathologic fractures is mere coincidental clinical manifestation. Fibro-osseous lesions of the head and neck. For the latest visit to cmeentoma clinic 2 months ago, the outcome in the neomandible region was desirable, and in parallel, the recent DEA test result took a favorable turn as BMD had increased to Apart from that, it is still debatable about the timing of surgical intervention for FGC patients.

The most famous case is of Novemthree Siahaan who died on September 15,a young Indonesian boy from Batam Island who received medical care in Haulien, Taiwan through a Buddhist missionary from the Tzu Chi Foundationwhich was documented on the Discovery Health Channel.

To sum up, our unusual radiographic and givantiform findings of FGC give rise to a renewed understanding and a broad change to the stereotypic definition.

CC ]. Among all the reports available, Rossbach et al 3 was the first to postulate the correlation of a brittle bone disorder with FGC. As a direct consequence, physical deterioration was also found by his giganhiform. Large vascular malformation in a child presenting with vascular steal phenomenon managed with pial synangiosis.


Suspicious of similar osseous problems in other anatomic locations, we then recommended a pelvic computer tomography CT scan to the patient.

Therefore, we agree with Noffke et al 14 and Finical 15 in resorting to a complete resection of FGC with curative purposes whenever feasible. Clinical Synopsis Toggle Dropdown. A The adolescent patient’s aunt who had received surgery nonvascularized iliac bone reconstruction 30 years ago now complaint of anterior maxillary mass with chronic infection. Undocumented radiographic changes and related bone metabolism disorder are herein hypothesized and discussed.

We present an adolescent case with recurrent familial gigantiform cementoma who received surgical intervention in our hospital. Arteriovenous malformation of the scalp with cerebral steal. From Wikipedia, the free encyclopedia. Showing of 15 references. In addition, FGC also carries a striking tendency toward more exuberant damilial with multiquadrant jaw involvement. Periprosthetic bone mineral density changes after unicondylar knee arthroplasty.

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Fibro-osseous familiial of the face and jaws. Gigantiform cementoma in a child. For sake of differential diagnosis with hyperparathyroidism-jaw tumor HPT-JT syndrome, 4 several laboratory analyses, which included serum parathyroid hormone PTHphosphate levels, calcium levels, and alkaline phosphatase ALP activity, were famioial accordingly. F 3-D computed gigantkform reconstruction of postoperative view. A The adolescent patient with a huge mass extending along the mandible body.

Prosthodontic treatment for edentulous patients, vol 1. Report of a case documented with computed tomography and 3D imaging. Besides, his pelvis was also considered to be susceptible to fractures because both cortical and trabecular bones were undergoing a progeric or osteopenic conversion signifying an unexpected calcium loss. Cemento-osseous dysplasia of the jaw bones: The authors report no conflicts of interest.

Closer examination of his family pedigree verified our concern of a long-standing phenomenon of multiple fractures accompanying FGC in jaws.

Familial Gigantiform Cementoma

From This Paper Figures, tables, and topics from this paper. Nevertheless, in terms of his description, the progression of disease and related underlying causes has not been clarified. Despite the paucity of information regarding FGC, DEA, as we believe, carries diagnostic and ce,entoma implications, along with other radiographic examinations.


Macdonald Oral surgery, oral medicine, oral pathology and…. Abstract Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. F Two bony defects were identified in reconstructed pelvic CT images. D Postoperative view of patient after bilateral mandibulectomy. In the family reported cementoa Young et al.

Familial gigantiform cementoma: classification and presentation of a large pedigree.

B Preoperative panorex X-ray showed a characteristic radiographic feature of familial gigantiform cementoma FGC with well-circumscribed radiopaque areas involving all quadrants of the jaw, with mandible being more severely damaged. The feasibility of using fibular flaps was ruled out in view of his unfortunate history of frequent lower-extremity fractures. Undocumented radiographic changes and related bone metabolism disorder are herein hypothesized and discussed.

NarayanWilfried Wagner Oral surgery, oral medicine, oral pathology and….

Compared with other 3 CODs, FGC takes on a really unique and aggressive form of behavior that is not supposed to be clinically approached in the existing framework of classification.

Surgical removal of the affected bone is needed, and has to be followed by reconstruction. This case report discusses the oral management and prosthetic rehabilitation of two patients presenting familial gigantiform cementoma with Ehlers-Danlos Syndrome.

Loss of lamina dura, decreased skull bone density, and sporadic bony defects all served as convincing evidence of the serious osseous fragility. His previous surgical history was remarkable and extensive. The lesions had an early age of onset and developed slowly.